Biliary atresia is a rare disease characterized by biliary obstruction which occurs during the perinatal period. It is the most common cause of neonatal cholestasis (biliary retention). The reported world incidence varies from 1/20 000 and 1/3 10
0 live births, Asia and Pacific countries being the most affected. It am
ounts to 1/18 000 live births in Europe. Girls are slightly more affected than boys. Biliary atresia is a non hereditary condition of unknown origin.
Illustration : Different types of biliary atresia, where bile conducts are partially or totally blocked or absent.